HIBCH report

I. Expression across cell types

II. Expression across tissues

III. Associated gene sets

GO_0006574Biological processvaline catabolic process
GO_0009083Biological processbranched-chain amino acid catabolic process
GO_0005759Cellular componentmitochondrial matrix
GO_0005739Cellular componentmitochondrion
GO_0016787Molecular functionhydrolase activity
GO_0003860Molecular function3-hydroxyisobutyryl-CoA hydrolase activity

IV. Literature review

[source]
Gene nameHIBCH
Protein name3-hydroxyisobutyryl-CoA hydrolase
3-hydroxyisobutyryl-CoA hydrolase (HIB-CoA hydrolase) (HIBYL-CoA-H) (EC 3.1.2.4) (3-hydroxyisobutyryl-coenzyme A hydrolase)
3-hydroxyisobutyryl-CoA hydrolase (EC 3.1.2.4)
3-hydroxyisobutyryl-CoA hydrolase, mitochondrial (EC 3.1.2.4) (3-hydroxyisobutyryl-coenzyme A hydrolase) (HIB-CoA hydrolase) (HIBYL-CoA-H)
Synonyms
DescriptionFUNCTION: Hydrolyzes 3-hydroxyisobutyryl-CoA (HIBYL-CoA), a saline catabolite. Has high activity toward isobutyryl-CoA. Could be an isobutyryl-CoA dehydrogenase that functions in valine catabolism. Also hydrolyzes 3-hydroxypropanoyl-CoA. .

FUNCTION: Hydrolyzes 3-hydroxyisobutyryl-CoA (HIBYL-CoA), a saline catabolite. Has high activity toward isobutyryl-CoA. Could be an isobutyryl-CoA dehydrogenase that functions in valine catabolism. Also hydrolyzes 3-hydroxypropanoyl-CoA. .

FUNCTION: Hydrolyzes 3-hydroxyisobutyryl-CoA (HIBYL-CoA), a saline catabolite. Has high activity toward isobutyryl-CoA. Could be an isobutyryl-CoA dehydrogenase that functions in valine catabolism. Also hydrolyzes 3-hydroxypropanoyl-CoA. .

FUNCTION: Hydrolyzes 3-hydroxyisobutyryl-CoA (HIBYL-CoA), a saline catabolite. Has high activity toward isobutyryl-CoA. Could be an isobutyryl-CoA dehydrogenase that functions in valine catabolism. Also hydrolyzes 3-hydroxypropanoyl-CoA. .

FUNCTION: Hydrolyzes 3-hydroxyisobutyryl-CoA (HIBYL-CoA), a saline catabolite. Has high activity toward isobutyryl-CoA. Could be an isobutyryl-CoA dehydrogenase that functions in valine catabolism. Also hydrolyzes 3-hydroxypropanoyl-CoA. .

AccessionsH7C126
ENST00000409934.1
B8ZZZ0
ENST00000399855.2
ENST00000359678.10 [Q6NVY1-1]
ENST00000392332.7 [Q6NVY1-2]
B9A058
ENST00000410045.5
ENST00000416732.5
ENST00000409820.2
ENST00000392333.7
H7BYI7
F8W8A6
H7C1A5
Q6NVY1